We report a rare case of sparganosis presented as cauda equina syndrome. Cauda equina syndrome secondary to extramedullary spinal sparganosis infection represents a diagnostic challenge. It should be carefully considered in the differential diagnosis of patients presenting similar characteristics. Although both medical and surgical treatments contribute to the management of this condition, in cases of neurologic deficit due to the mass effect of the lesion, urgent surgical decompression should be attempted to prevent further worsening of the neurological condition.