| 摘要 |
Isolated mesenteric fibromatosis is a rare disease with characteristics of large tumor mass associated with relatively few clinical symptoms, localized tumor infiltration and no relation with other disease. This is a report of two cases of isolated mesenteric fibromatosis, surgically identified, at the mesentery of the ileum. Both patients presented with abdominal pain and mass. There has been no evidence of recurrence after a long follow-up period (seven and five years, respectively). The tumor often appears during the fourth decade of life and is more common in men than in women. The ileum is most commonly involved. The etiology is still unclear, and clinical symptoms are usually non-specific. The lesion may appear as an asymptomatic or slightly painful abdominal mass. G-I tract bleeding and acute abdomen from bowel perforation are other common symptoms. Occasionally, the condition may present as an incidental finding during laparotomy for some other reason. Computer tomography scan of the abdomen is considered to be the most useful diagnostic modality, and can often localize
the tumor well. The mainstay treatment is surgical excision. Although the tumor will not metastasize, it can recur locally and it may lead to death. In summary, isolated mesenteric fibromatosis is a relative benign tumor, with generally good prognosis if resection is complete. |
