| 篇名 |
Multicentric Malignant Peripheral Nerve Sheath Tumors of Small Intestine and Thigh: Report of a Case |
| 作者 |
Chi-Hsuan Lin, Jung-Liang Kao, Ping-Hung Huang, Chih-Wei Kuo |
| 卷期/出版年月 |
43卷5期 (2010/10) |
| 頁次 |
262-266 |
| 摘要 |
Abstract Primary malignant peripheral nerve sheath tumor (MPNST) of the small
bowel is an extremely rare disease. We report a multicentric MPNSTs of the left
thigh and jejunum in a 59-year-old male, who visited our hospital twice in seven
months because of a subcutaneous lump on the posterior aspect of the left thigh and
life-threatening melena respectively. Laparotomy was performed for the small bowel
tumor and a segment of the jejunum containing the tumor near its midportion was
resected with end-to-end jejunojejunostomy. Histologically, the tumor which had
been excised seven months previously was diagnosed as classical MPNST occurring
in the left thigh, and that resected this time, as epithelioid MPNST occurring in the
jejunum. Distant metastasis to multiple organs occurred one month after resection
of the jejunal MPNST, and the patient died three months later. This is the first case
of an MPNST arising in the small intestine reported in Taiwan. |
| 關鍵詞 |
malignant peripheral nerve sheath tumor, multicentric tumors, small bowel malignancy |
| 分類 |
Case Report |
